Common name

IUPAC name

(3R)-3-hydroxy-4-(trimethylazaniumyl)butanoate

SMILES

C[N+](C)(C)C[C@H](O)CC([O-])=O

Compound class

Vitamin B Complex; Dietary Supplements; Alimentary Tract and Metabolism; Amino Acids and Derivatives;

Therapeutic area

For treatment of primary systemic carnitine deficiency, a genetic impairment of normal biosynthesis or utilization of levocarnitine from dietary sources, or for the treatment of secondary carnitine deficiency resulting from an inborn error of metabolism such as glutaric aciduria II, methyl malonic aciduria, propionic acidemia, and medium chain fatty acylCoA dehydrogenase deficiency. Used therapeutically to stimulate gastric and pancreatic secretions and in the treatment of hyperlipoproteinemias. Parenteral levocarnitine is indicated for the prevention and treatment of carnitine deficiency in patients with end-stage renal disease.